Name | sapropterin dihydrochloride |
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Synonyms |
(6R)-2-amino-6-[(1R,2S)-1,2-dihydroxypropyl]-5,6,7,8-tetrahydropteridin-4(1H)-one dihydrochloride
(6R,1'R,2'S)-6-(1',2'-dihydroxypropyl)-5,6,7,8-tetrahydrobiopterin Dapropterin (6R)-2-Amino-6-[(1R,2S)-1,2-dihydroxypropyl]-5,6,7,8-tetrahydro-4(1H)-pteridinone (6R)-5,6,7,8-tetrahydro-L-biopterin (6R)-Tetrahydrobiopterin 6R-tetahydrobiopterin Dapropterin dihydrochloride Biopten (6R)-5,6,7,8-TETRAHYDRO-L-BIOPTERIN DIHYDROCHLORIDE 4(1H)-Pteridinone, 2-amino-6-[(1R,2S)-1,2-dihydroxypropyl]-5,6,7,8-tetrahydro-, (6R)-, hydrochloride (1:2) sapropterinum (6R)-2-Amino-6-[(1R,2S)-1,2-dihydroxypropyl]-5,6,7,8-tetrahydropteridin-4(1H)-one R-THBP MFCD00891665 (R)-2-Amino-6-((1R,2S)-1,2-dihydroxypropyl)-5,6,7,8-tetrahydropteridin-4(3H)-one dihydrochloride (6R)-5,6,7,8-Tetrahydrobiopterin (6R)-tetrahydrobiopterin dihydrochloride 4(1H)-Pteridinone, 2-amino-6-[(1R,2S)-1,2-dihydroxypropyl]-5,6,7,8-tetrahydro-, (6R)- [6R-[6R*(1R*,2S*)]]-2-amino-6-(1,2-dihydroxypropyl)-5,6,7,8-tetrahydro-4(1H)-pteridinone (6R)-Tetrahydrobiopterin hydrochloride (6R)-2-Amino-6-[(1R,2S)-1,2-dihydroxypropyl]-5,6,7,8-tetrahydro-4(1H)-pteridinone dihydrochloride Sapropterin kuvan (6R)-5,6,7,8-Tetrahydrobiopterin dihydrochloride 6b-5,6,7,8-Tetrahydro-L-biopterin (6R)-2-amino-6-[(1R,2S)-1,2-dihydroxypropyl]-5,6,7,8-tetrahydro-1H-pteridin-4-one,dihydrochloride 6R-Tetrahydro-L-biopterin (6R-(6R*(1R*,2S*)))-5,6,7,8-Tetrahydro-2-amino-6-(1,2-dihydroxypropyl)-4(1H)-pteridinone dihydrochloride R-THBP6R-BH4 (6R)-L-erythro-5,6,7,8-Tetrahydrobiopterin sapropterina (6R)-L-erythro-Tetrahydrobiopterin 4(1H)-pteridinone, 2-amino-6-[(1R,2S)-1,2-dihydroxypropyl]-5,6,7,8-tetrahydro-, (6R)-, dihydrochloride Sapropterin dihydrochloride Sapropterin (dihydrochloride) |
Description | Sapropterin dihydrochloride is a synthetic form of BH4 that is approved for the treatment of BH4 responsive PKU. (1) Sapropterin dihydrochloride can stimulate TH and TPH activities leading to improved dopamine and serotonin synthesis despite persistently elevated brain phenylalanine.(2) Sapropterin dihydrochloride is used to lower blood phenylalanine levels in tetrahydrobiopterin-responsive phenylketonuria in conjunction with a phenylalanine-restricted diet. |
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Related Catalog | |
References |
Density | 1.9±0.1 g/cm3 |
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Boiling Point | 506.6±60.0 °C at 760 mmHg |
Molecular Formula | C9H17Cl2N5O3 |
Molecular Weight | 314.17 |
Flash Point | 260.2±32.9 °C |
PSA | 136.29000 |
LogP | -4.22 |
Vapour Pressure | 0.0±3.0 mmHg at 25°C |
Index of Refraction | 1.822 |
Storage condition | −20°C |
CHEMICAL IDENTIFICATION
HEALTH HAZARD DATAACUTE TOXICITY DATA
|
Symbol |
GHS07 |
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Signal Word | Warning |
Hazard Statements | H302 |
Hazard Codes | Xn |
Risk Phrases | R22 |
RIDADR | NONH for all modes of transport |
WGK Germany | 3 |
RTECS | UO3516500 |
HS Code | 2933990090 |
~% 69056-38-8 69056-38-8 |
Literature: Australian Journal of Chemistry, , vol. 35, # 4 p. 785 - 793 |
Precursor 1 | |
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DownStream 0 |
HS Code | 2933990090 |
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Summary | 2933990090. heterocyclic compounds with nitrogen hetero-atom(s) only. VAT:17.0%. Tax rebate rate:13.0%. . MFN tariff:6.5%. General tariff:20.0% |